Propinol-L-Carnitine

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Cat. No.: 66270 Category:

Description

CAS #

20064-19-1

Concentration

98.00%

Description

Propinol-L-Carnitine is present in high abundance in the urine of patients with Methylmalonyl-CoA mutase (MUT) deficiency, together with Methylmalonic acid. MUT is a mitochondrial enzyme that catalyzes the isomerization of methylmalonyl-CoA to succinyl-CoA.

Keywords

(2R)-3-Carboxy-N,N,N-trimethyl-2-(1-oxopropoxy)-1-propanaminium inner salt, L-Carnitine propionyl ester, C3-Carnitine, Propanoyl-L-carnitine

Additional information

Size

10mg, 50mg